Table 1 : Anatomic classification of Ebstein anomaly [10].


Anatomic type Characterization

Type I Minimal displacement of the tricuspid valve with an adequate size right ventricle
Patients often remain asymptomatic until adulthood

Type II Marked displacement of the tricuspid valve and the functional right ventricle is small
Anterior leaflet is mobile

Type III Anterior leaflet is restricted

Type IV Displacement of the tricuspid valve is so severe that the right ventricle is absent and
the patients present in neonatal life with cyanosis

Stergiopoulos et al.Cardiovascular System  2015 3:7DOI : 10.7243/2052-4358-3-7