Table 3 : Management in adult Ebstein anomaly patients.


  • Diuretics for treatment of peripheral edema and right heart failure
  • Consider surgical intervention
  • Monitor for arrhythmias
  • Anticoagulation with warfarin for paradoxical embolus or atrial arrhythmias
  • Antibiotic prophylaxis before dental procedures is reasonable in cyanotic patients and postoperative patients with a prosthetic valve*
  • Routine follow up with a specialist in adult congenital heart disease
  • Counseling in women of childbearing potential regarding risks of pregnancy

*Antibiotic prophylaxis is usually not necessary in the unoperated, acyanotic patient.

Stergiopoulos et al.Cardiovascular System  2015 3:7DOI : 10.7243/2052-4358-3-7