Table 1 : Characteristics of the present cases and those described in the literature.


Patient Sex Reference Age*
(years)
Type of SS Time interval** Type of
leukaemia
Outcome

1 F Patient #1 72 Possible SS concomitant AML Death
2 M Patient #2 65 Possible SS concomitant AML Death
3 F [15] 59 AECC, primary 11 years AML ?
4 F [16] 53 AECC, primary 2 years AML Death
5 M [17] 55 AECC, primary 7 years ALL ?
6 M [18] 43 AECC, primary 5 years ALL ?

F: female; M: male; SS: Sjögren’s syndrome; AECC: American-European Consensus Conference; AML: acute myeloid leukaemia;
ALL: acute lymphoid leukaemia. *Age at diagnosis of SS.
** Time interval between the diagnosis of SS and the emergence of acute leukaemia.

Brault et al.Hematology and Leukemia  2017 5:2DOI : 10.7243/2052-434X-5-2