Cardiovascular System

Cardiovascular System

ISSN 2052-4358
Case report

An unusual finding of left ventriculography in Marfan syndrome with severe mitral valve prolapse

Masato Kimura1*, Ryo Takahashi1, Eichiro Kawai1, Takehiko Ohnoki1, Osamu Adachi2, Yoshikatsu Saiki2 and Shigeo Kure1

*Correspondence: Masato Kimura

1. Department of Pediatrics, Tohoku University School of Medicine, Sendai, Miyagi 980-8574, Japan.

Author Affiliations

2. Division of Cardiovascular Surgery, Tohoku University School of Medicine, Sendai, Miyagi 980-8574, Japan.

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A 16-year-old boy with Marfan syndrome was scheduled for open-heart surgery for dilated aortic sinuses of Valsalva. Preoperative cardiac catheterization with left ventricular angiography demonstrated bulging at the junction of the mitral annulus with an appearance like ‘a swim ring’. Transthoracic echocardiography showed severe mitral prolapse with the mitral valve leaflets rising toward the left atrium and stretching of the chordae tendineae. ECG-gated contrast CT revealed that this bulging was not the left ventricle itself but the interspace between the base of the left ventricle and mitral valve leaflets. This bulging disappeared after mitral valve plasty with an annuloplasty ring. This unusual finding might herald chordae tendinae rupture in Marfan syndrome.

Keywords: Marfan syndrome, mitral valve prolapse, left ventriculography, chordae tendinae rupture

ISSN 2052-4358
Volume 3
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